Hereditary benign telangiectasia?

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Şinasi Özsoylu

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Hereditary benign Telangiectasia: Report of 6 cases in a family

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Hereditary benign telangiectasia (HBT), first described in 1971,1 is a rare autosomal dominant disorder.2' 3, 4 It is characterised by widespread telangiectases which may be punctate, plaquelike, radiating or merely a diffuse blush. The lesions generally are observed before adolescence, and rarely during the first year of life.5 It is important to recognise HBT as it may only cause cosmetic dis...

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